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KMID : 0882420100790060705
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Korean Journal of Medicine
2010 Volume.79 No. 6 p.705 ~ p.709
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Concurrent renal and hepatic angiomyolipoma with pulmonary involvement in two patients with tuberous sclerosis
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Sung Ji-Yoon
Na Sun-Young
Jung Ji-Yong
Lee Hyun-Hee
Jung Woo-Kyung
Sung Yon-Mi
Chang Jae-Hyun
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Abstract
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Tuberous sclerosis (TS) involves multiple organs. Angiomyolipoma of the liver or kidney is one of the clinical manifestations of TS. However, coexistent renal and hepatic angiomyolipoma associated with TS is a rare condition. Pulmonary involvement is extremely rare, and occurs in only 0.1~1% of TS. We report two cases of concurrent renal and hepatic angiomyolipomas with pulmonary involvement in patients with TS. The first case was a 35 year-old woman who showed multiple angiomyolipomas in the liver and both kidneys and cystic parenchymal changes in the lungs. The other case was a 27-year-old woman who showed multiple angiomyolipomas in the liver and both kidneys, and multinodular pulmonary shadows. To the best of our knowledge, this is the first reported case of renal and hepatic angiomyolipomas associated with pulmonary involvement in Korea.
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KEYWORD
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Angiomyolipoma, Tuberous sclerosis, Lymphangioleiomyomatosis, Multifocal micronodular pneumocyte hyperplasia
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